The Robinow syndrome is an extremely rare congenital syndrome that causes facial malformations, as well as genital, cardiac and skeletal abnormalities. Patients with this syndrome undergo several operations during their life. Because of the facial abnormalities they carry a potential risk for difficult intubation. We describe the case of a boy who underwent several operations with documented difficult intubation. The laryngeal mask airway provided a good solution for airway control and afforded adequate ventilation under both controlled mechanical ventilation and spontaneous breathing.

The laryngeal mask airway effectively provided airway control and adequate ventilation for a boy with the rare congenital Robinow syndrome, despite difficult intubation.

Laryngeal mask airway and the Robinow syndrome.

Key Takeaway: The laryngeal mask airway effectively provided airway control and adequate ventilation for a boy with the rare congenital Robinow syndrome, despite difficult intubation.